Anaesthetic Management of Upper Limb Fracture in a Patient With Cleidocranial Dysplasia

Abstract

Background: Cleidocranial dysplasia (CCD) is a rare autosomal dominant skeletal disorder which is characterised by defective skeletal ossification, mainly affecting the clavicles and skull, along with dental abnormalities. Case

Presentation: This study reports the anaesthetic management of a 12 year old boy with cleodocranial dysplasia with traumatic fracture of both bone right forearm without any neurovascular deficits. Ultrasound guided Supraclavicular brachial plexus block was administered under intravenous sedation. Vitals were monitored throughout the case which was stable and surgery was completed.  

Conclusion: Considering the ease, safety and potency of ultrasound guided supraclavicular block, it may be used for patients with CCD with absent clavicle. Peripheral nerve block under intravenous sedation avoids airway manipulation in patients with CCD characterized by generalised skeletal and orofacial defects.